LES HÉMANGIOBLASTOMES DE LA FOSSE CÉRÉBRALE POSTÉRIEURE (à propos de 21 cas)

Abstract

Hemangioblastomas are benign vascular tumors of the central nervous system that can occur sporadically or as part of Von Hippel Lindau disease (VHL). The study of the 21 cases of hemangioblastomas collected in the Neurosurgery Department of CHU IBN ROCHD Annaba involves a pure infratentorial involvement. No localization in the rest of the neuraxis or visceral has been detected. All the patients had a sporadic hemangioblastoma. The clinical picture is dominated by the syndrome of increased intracranial pressure (ICP) and the cerebellar syndrome, and in all cases, it was the increased ICP that was the initial revelation. MRI and CT are the two preferred paraclinical methods: MRI is more sensitive in revealing the presence of the tumor, its characteristics (location, size, volume, exact number...) and the localization of the cystic portion of the tumor, its relationship with the mural nodule as well as its repercussions on the ventricular cavities. The diagnosis of infratentorial hemangioblastoma has a poor prognosis due to postoperative mortality, the risk of recurrence, and multiple locations. The treatment consists of as complete a tumor removal as possible, and the diversion of associated hydrocephalus can be discussed in certain cases. Post-operative monitoring is carried out using MRI, which can detect a recurrence by revealing a cyst or ventricular dilation. Finally, in individuals with a family history of Von Hippel Lindau disease, it would not be excessive to conduct periodic ophthalmic examinations and brain MRIs